What is solitary fibrous tumor of the pleura?
Background: The solitary fibrous tumor of the pleura (SFTP) is a rare primary tumor arising from mesenchymal cells in the areolar tissue subjacent to the mesothelial-lined pleura. Only about 800 cases have been reported in the medical literature.
What is the most common pleural tumor?
The most common pleural tumor is metastatic cancer, which usually causes pleural effusion with tumor nodules. Common cancers that metastasize to the pleural space include lung, breast, and gastrointestinal primary carcinomas (1).
How rare is solitary fibrous tumor?
Introduction. Solitary fibrous tumor (SFT) is a rare soft tissue neoplasm, with an incidence of about 0,2/100.000/years. It was called “haemangiopericytoma” by Stout and Murray in 1942.
What is a pleural fibroma?
Pleural fibromas, also known as localized fibrous tumors of the pleura or benign mesothelioma, are rare tumors that arise from the pleura [1]. 80% of them originate in the visceral pleural [2].
What is DPS disease?
Doege-Potter syndrome (DPS), a paraneoplastic syndrome, presents as a hypoinsulinemic hypoglycemia from the ectopic secretion of insulin-like growth factor II from a solitary fibrous tumor which may be intrapleural or extrapleural in origin.
What is a pleural mass?
What are Pleural Tumors? Pleural tumors are found in the pleural space—the cavity between the lungs and chest wall that contains lubricating pleural fluid. A pleural tumor is almost always metastatic (cancerous) and difficult to operate on.
Can the pleura be removed?
Pleurectomy is a type of surgery in which part of the pleura is removed. This procedure helps to prevent fluid from collecting in the affected area and is used for the treatment of mesothelioma, a pleural mesothelial cancer.
How long can you live with pleural effusion?
Malignant pleural effusion (MPE) is a common but serious condition that is related with poor quality of life, morbidity and mortality. Its incidence and associated healthcare costs are rising and its management remains palliative, with median survival ranging from 3 to 12 months.
Are solitary fibrous tumors malignant?
Most solitary fibrous tumors are noncancerous (benign), but in rare cases, solitary fibrous tumors can be cancerous (malignant). Solitary fibrous tumors tend to grow slowly and may not cause signs and symptoms until they become very large.
Is a solitary fibrous tumor a sarcoma?
Background. Solitary fibrous tumour (SFT) is a rare soft tissue sarcoma with a low metastatic potential.
Can a pleural mass be benign?
Pleural lipomas are benign, slow-growing tumors that arise from fat cells present in the pleural lining. They are well circumscribed, small tumors but can grow to large sizes leading to compressive symptoms.
